Anti-GCSH抗體說明,*裂解系統(tǒng)H蛋白抗體介紹:GCSH is a 173 amino acid mitochondrial protein that contains one lipoyl-binding domain and belongs to the gcvH family. Defects in the gene encoding GCSH are the cause of glycine encephalopathy (GCE), an autosomal recessive disease that is also referred to as non-ketotic hyperglycinemia (NKH). Characterized by severe neurological symptoms, patients with GCE have a large amount of glycine accumulated in their body fluids. The gene encoding GCSH maps to human chromosome 16, which encodes over 900 genes and comprises nearly 3% of the human genome.
相關(guān)的標(biāo)記有:Alexa Fluor 350 標(biāo)記、Alexa Fluor 488 標(biāo)記、Alexa Fluor 555 標(biāo)記、Alexa Fluor 647 標(biāo)記、AP標(biāo)記、APC標(biāo)記、Biotin標(biāo)記、Cy3標(biāo)記、Cy5標(biāo)記、Cy5.5標(biāo)記、Cy7標(biāo)記、FITC標(biāo)記、Gold標(biāo)記、HRP標(biāo)記、PE標(biāo)記、PE-Cy3標(biāo)記、PE-CY5標(biāo)記、PE-CY5.5標(biāo)記、PE-CY7標(biāo)記、RBITC標(biāo)記
保存條件:Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹:
產(chǎn)品名稱:Anti-GCSH抗體說明,*裂解系統(tǒng)H蛋白抗體
產(chǎn)品編號:BYK-13323R
英文名稱 GCSH
中文名稱 *裂解系統(tǒng)H蛋白抗體
別 名 GCE; GCSH; GCSH_HUMAN; Glycine cleavage system H protein; Glycine cleavage system H protein mitochondrial; Glycine cleavage system protein H (aminomethyl carrier); Glycine cleavage system protein H; Lipoic acid containing protein; mitochondrial; Mitochondrial glycine cleavage system H protein; NKH.
研究領(lǐng)域 腫瘤 細(xì)胞生物 信號轉(zhuǎn)導(dǎo) 細(xì)胞類型標(biāo)志物 新陳代謝
產(chǎn)品價(jià)格:詢價(jià)(電詢或客服)
抗體來源:本公司抗體有兔來源和鼠來源等
克隆類型:兔來源為多抗,鼠來源為單抗
產(chǎn)品類型:一抗
產(chǎn)品用途:科研實(shí)驗(yàn)
性 狀: Lyophilized or Liquid
濃 度: 1mg/1ml
亞 型: IgG
貯 存: 貯存于-20℃.
相關(guān)產(chǎn)品:
Anti-CR (Calretinin) 鈣結(jié)合蛋白抗體
Anti-SLAMF6/LY108(SLAM family member 6 precursor) SLAMF6抗體
Anti-CRMP2/CRAM(collapsin response mediator protein-2) 抗二氫嘧啶酶樣2抗體
Anti-CRLR/CALCRL(calcitonin receptor like precursor) 降鈣素受體樣蛋白抗體
Anti-SLAMF7/CRACC/CD319 SLAMF7抗體
Anti-CRP (C-reactive protin) C-反應(yīng)蛋白抗體
Anti-CRP(C-reactive protin) 鼠抗人C-反應(yīng)蛋白單克隆抗體
Anti-CREB-1(cAMP responsive element binding protein-1) 環(huán)腺苷酸應(yīng)答元件結(jié)合蛋白抗體
Anti-CREB-1(cAMP responsive element binding protein-1) 環(huán)腺苷酸應(yīng)答元件結(jié)合蛋白抗體
Anti-cRaf/Raf1(c-raf 1) 抗cRaf/Raf1抗體
Anti-phospho-CREB-1 (pSer133) 磷酸化環(huán)腺苷酸應(yīng)答元件結(jié)合蛋白抗體
Anti-CRF/CRH (Corticotropin-Releasing Factor/hormone) 促腎上腺皮質(zhì)激素釋放因子
Anti-CRF/CRH (Corticotropin-Releasing Factor) 促腎上腺皮質(zhì)激素釋放因子抗體
Anti-CSIG(cellular senescence inhibited gene) 細(xì)胞衰老抑制基因抗體
Anti-Cripto-1(NT) 畸胎瘤衍化生長因子抗體(表皮生長因子相關(guān)肽)N端
Anti-Cripto-1(C-Terminus) 畸胎瘤衍化生長因子抗體(表皮生長因子相關(guān)肽)C端
優(yōu)貨供應(yīng),更多優(yōu)質(zhì)產(chǎn)品
人天*轉(zhuǎn)氨酶/谷草轉(zhuǎn)氨酶(GOT/GPT)ELISA試劑盒
人抗乙型肝炎病毒核心抗體(HBcAb)ELISA試劑盒
人抗乙型肝炎病毒核心IgM抗體(HBcAb-IgM)ELISA試劑盒
人抗乙型肝炎病毒核心IgG抗體(HBcAb-IgG)ELISA試劑盒
人抗乙型肝炎病毒表面抗體(HBsAb)ELISA試劑盒
人抗乙型肝炎病毒e抗體(HBeAb)ELISA試劑盒
人抗巨細(xì)胞病毒抗體IgM(anti-CMV IgM)ELISA試劑盒
人抗甲型肝炎病毒IgM抗體(anti-HAV)ELISA試劑盒
人抗甲型肝炎病毒IgG抗體(anti-HAV)ELISA試劑盒
人抗弓形體IgM抗體(anti-tox IgM)ELISA試劑盒